Manifestaciones otorrinolaringologicas en pacientes con. Wegeners granulomatosis is a rare systemic vasculitis, whose. Granulomatosis with polyangiitis gpa, previously known as wegeners granulomatosis wg, is an extremely rare longterm systemic disorder that involves the formation of granulomas and inflammation of blood vessels vasculitis. Wegeners granulomatosis is a rare systemic vasculitis, whose etiopathogenic substrate is the inflammation of the blood vessels, preventing the free circulation of blood flow. Granulomatosis con poliangitis sintomas y causas mayo clinic. It is a multisystemic autoimmune disorder characterized by necrotizing granulomatous inflammation, necrotizing tissue and various grades of vasculitis. Wegeners granulomatosis wg is a type of systemic granulomatous vasculitis primarily affecting the respiratory tract and kidneys find. Clinically it is characterized by the presence of respiratory, nasal, auditory and renal. Ernesto cairoli, ricardo silvarino, enrique mendez. Hum pathol glomerular vascular cell adhesion molecule1 expression in renal vasculitis. The respiratory system is most commonly affected in limited forms of the disease, however upper. Granulomatosis with polyangiitis gpa, formerly known as wegeners granulomatosis is an autoimmune small vessel vasculitis which is highly associated with antineutrophil cytoplasmic antibodies anca. Granulomatosis con poliangeitis genetic and rare diseases.